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Cystic meningioangiomatosis in neurofibromatosis type 2: an MRI–pathological study

¹ Department of Neurology, Austin Health, Heidelberg, Victoria 3084, ² Clinical School, The University of Melbourne, Austin Health, Heidelberg, Victoria 3084, ³ Departments of Anatomical Pathology and, ⁴ Radiology, Austin Health, Heidelberg, Victoria 3084,, ⁵ Department of Radiology, The University of Melbourne, Parkville, Victoria 3052, Australia

Correspondence: L Anne Mitchell, Department of Radiology, Austin Health, Heidelberg, Victoria 3084, Australia. E-mail: anne.mitchell{at}austin.org.au

We report cerebral cystic meningioangiomatosis in a patient with neurofibromatosis type 2. An 18-year-old woman presented with progressive hemiparesis secondary to a meningioma at the foramen magnum. Her MR examination also demonstrated three small cortical and subcortical cystic lesions. She underwent surgery for the meningioma, but died from brainstem infarction. Post-mortem histopathological examination of the cystic lesions showed enlarged subcortical perivascular spaces with overlying meningioangiomatosis. The unusual features and possible pathogenesis are discussed.