This Article Figures Only Full Text Full Text (PDF) Services Similar articles in this journal Similar articles in PubMed Alert me to new issues of the journal Download to citation manager Citing Articles Citing Articles via Google Scholar Google Scholar Articles by REIS, C Articles by SOM, P M Search for Related Content PubMed PubMed Citation Articles by REIS, C Articles by SOM, P M

A rare spontaneous osteosarcoma of the calvarium in a patient with long-standing fibrous dysplasia: CT and MR findings

¹ Department of Neuroradiology, S. João University Hospital, Porto, Portugal, and the Departments of ² Otolaryngology, ³ Neurosurgery and ⁴ Radiology, Mount Sinai School of Medicine, New York University, New York, USA

Correspondence: Dr Carina Reis, Alameda Prof. Hernani Monteiro, Porto, 4204-451 Porto, Portugal. E-mail: reis_carina{at}yahoo.com

A 52-year-old man with long-standing craniofacial polyostotic fibrous dysplasia (FD) and no history of prior radiation therapy developed a spontaneous right temporal bone osteosarcoma. Such spontaneous sarcomatous degeneration of FD is rare, particularly in the calvarium/skull, where, to our knowledge, only six prior cases have been reported in the literature. We report this case because it is a rare entity with well-documented CT and MR images, and to emphasize the importance of depicting imaging features of sarcomatous degeneration among the complex imaging findings of FD.